Certified Registered Nurse Anesthetist (CRNA) Practice Exam

Is fusion of the cervical spines a feature of Pierre-Robin syndrome?

1. Yes, it is a common feature

2. No, it is not a feature of Pierre-Robin syndrome

3. Only in severe cases of Pierre-Robin syndrome

4. It's a rare occurrence in Pierre-Robin syndrome

The correct answer is: No, it is not a feature of Pierre-Robin syndrome

The connection between Pierre-Robin syndrome and cervical spine fusion is not established, which makes the selected answer accurate. Pierre-Robin syndrome primarily involves a set of congenital malformations, notably characterized by micrognathia (a small jaw), glossoptosis (a displaced tongue), and cleft palate. These features lead to breathing and feeding difficulties, particularly in infants. While there is a range of associated anomalies in individuals with Pierre-Robin syndrome, fusion of the cervical spine does not typically factor into the syndrome's presentation. Conditions like cervical spine fusion can be associated with other syndromes or congenital issues, but they are not inherent features of Pierre-Robin syndrome. Thus, stating that fusion is not a feature accurately reflects the current understanding of the syndrome's clinical profile and supports the reliability of the answer provided.